To study the clinical features, diagnosis and therapy of hydroa vacciniforme-like cutaneous T cell lymphoma.
METHODS:
The clinical presentations and the findings of laboratory examinations and skin biopsy of affected tissue in a child with hydroa vacciniforme-like cutaneous T cell lymphoma were retrospectively reviewed.
RESULTS:
The child manifested as rash, fever and lymph node intumesce. Rash was pantomorphia, including edematous erythema, vesicles, crusts, necrosis and depressed scar, and it was mild in winter and severe in summer, mainly involving in the face and extremities. Epstein-Barre vivus (EBV)-IgM was positive. Histopathological findings revealed focal lymphocyte invasion in subcutaneous panniculus adiposus. The clinical symptoms were improved after glucocorticoid treatment in this child.
CONCLUSIONS:
Hydroa vacciniforme-like cutaneous T cell lymphoma has special clinical manifestations. This disorder may be definitely diagnosed by skin biopsy of affected tissue and immunohistochemistry assay. Glucocorticoid treatment is effective. EBV infection may be related to the development of this disorder.
Hydroa vacciniforme-like cutaneous T cell lymphoma: a case report and literature review
Zhongguo Dang Dai Er Ke Za Zhi. 2009 Jul; 11(7): 596-8Li HY, Wang HL, Gao TZ, Zhuo ZH, Li DM, Li H (Hubmed.org)
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METHODS:
The clinical presentations and the findings of laboratory examinations and skin biopsy of affected tissue in a child with hydroa vacciniforme-like cutaneous T cell lymphoma were retrospectively reviewed.
RESULTS:
The child manifested as rash, fever and lymph node intumesce. Rash was pantomorphia, including edematous erythema, vesicles, crusts, necrosis and depressed scar, and it was mild in winter and severe in summer, mainly involving in the face and extremities. Epstein-Barre vivus (EBV)-IgM was positive. Histopathological findings revealed focal lymphocyte invasion in subcutaneous panniculus adiposus. The clinical symptoms were improved after glucocorticoid treatment in this child.
CONCLUSIONS:
Hydroa vacciniforme-like cutaneous T cell lymphoma has special clinical manifestations. This disorder may be definitely diagnosed by skin biopsy of affected tissue and immunohistochemistry assay. Glucocorticoid treatment is effective. EBV infection may be related to the development of this disorder.
Hydroa vacciniforme-like cutaneous T cell lymphoma: a case report and literature review
Zhongguo Dang Dai Er Ke Za Zhi. 2009 Jul; 11(7): 596-8Li HY, Wang HL, Gao TZ, Zhuo ZH, Li DM, Li H (Hubmed.org)
Related:
Cutaneous Lymphoma And Mycosis Fungoides, Mycosis Definition
Fatal cytotoxic cutaneous lymphoma presenting as ulcerative psoriasis.
Lymphoma society - cutaneous lymphoma foundationnon
Cutaneous lymphoma: one patient's story
T-cell cutaneous lymphoma staging
Cutaneous Lymphoma
Stem cell transplant effective cure for refractory cutaneous lymphoma
Malignant Cutaneous Tumors: Cutaneous Lymphoma
Cutaneous lymphoma incidence patterns in the United States
